CLEFT LIP
- Failure of the maxillary & median nasal process to fuse
- Congenital deformity. Common among males
- Several staggered suture line to minimize notching
SIGNS & SYMPTOMS
- Difficulty in feeding
- Mouth breathing - air & infxn
SURGICAL TREATMENT: Ideal is 6 - 12weeks old
- Surgical Readiness: 10 wks old, 10 g of Hgb, at least 10 lbs., <>
- Procedure: close the defect called Cheiloplasty
PRE-OP
- Feeding Technique: Dropper with SAP
POST-OP
- Position: SUPINE never Prone (No head control)
- Promote Arm & Elbow Restraint
- Prevent Tension on suture lines: Anticipate the needs to avoid crying. Use of Logan’s Device (Bow / Bar)
- Anticipate Respiratory distress due to swelling of post-op area.
- Clean the suture line after feeding: sterile water or CBW
CLEFT PALATE
- Midline Fissure on the HARD PALATE. Most common in FEMALES.
- SURGICAL TREATMENT: Done before speech development begins
- Procedure: Palatoplasty
PRE-OP
- Feeding: flange nipple, lamb’s nipple, Brecht Feeder
- Breastfeeding method: With use of Palatar prosthesis
POST-OP
- Feeding device and Diet: Breast milk (by breast), commercial nipple, or from a cup. Never use a Straw because it can hit suture. Use blender for soft diet.
- Position: Prone (Abdomen or side) to promote natural drainage of secretion.
- Observe for bleeding: frequent swallowing.
- Use of elbow restraint to protect suture lines (cardboard on elbow → avoid flexion).
GASTRO ESOPHAGEAL REFLUX (GER) / CHALASIA
- Movement of gastric (acidic) contents to the esophagus
- Thicken milk
- Positioning: Upright position when feeding.
- Burp after feeding to eliminate air bubbles in stomach.
- If position is supine: Turn Right Lateral ( semi-upright ) - promote absorption by the Small Intestine (SI).
- H2 antagonist given to reduce acid & prevent esophagitis.
- Proton pump inhibitor, Omeprazole, Lansoprazole : blocks acid production
If not resolved within One (1) year, Cardiac Sphincter surgery is done. - Wrapping (tighten, 360 degrees) of Fundal part of the stomach to the distal esophagus.
- This surgery is called: NISSEN FUNDOPLICATION
PYLORIC STENOSIS
There is a narrowing or tightening of the Pyloric Sphincter. Food is blocked → Small Intestine → Food is regurgitated back to esophagus. It occurs around 1- 10 weeks of age. Most common in Males.
SIGNS & SYMPTOMS:
- Abdominal distention (visible peristalsis)
- Vomiting (non-bile stained)
- Projectile vomiting (4 – 6 weeks)
- Palpable olive shaped mass in RUQ.
- Constipation
DIAGNOSIS:
- Barium Swallow: X-ray reveals a String Sign or appearance
SURGICAL TREATMENT
- PYLOROMYOTOMY: The procedure is called FREDET – RAMSTEDT PROCEDURE
a. Involves first a LAPAROTOMY
b. Next is LAPAROSCOPY
PRE-OP
- Correct the existing Fluid & Electrolyte Imbalance (FEI), IVF for dehydration. KCl for Hypokalemia & Alkalosis.
- Correct Nutritional Balance: TPN as needed / thickened formula.
POST-OP
- Feeding is begun 4 – 6 hrs. post-op, small frequent & slow feedings. Full feeding at 48 hrs. post-op.
- Burp the infant.
- High Fowler’s position during feeding & place at right – lateral after burping.
TRACHEOESOPHAGEAL FISTULA (TEF) / ATRESIA OF THE ESOPHAGUS
- Esophagus in front of trachea
- Connect esophagus w/ trachea
1. Esophagus didn’t connect to stomach
2. Esophagus twist, food can’t do down - 5 TYPES OF TEF
A. B. C. D. E.
MOST COMMON: Type C
- Upper end esophagus blind pouch
- Lower end esophagus connect to trachea
BOTH CONNECTED TRACHEA:
- Upper end esophagus
- Lower end esophagus
MANIFESTATIONS OF ASPIRATION (3 C’s)
- Cough, Choking, Cyanosis
- Problem: Aspiration & Nutrition
NURSING DIAGNOSIS
- Potential for injury related to ABN connection between esophagus & Trachea
Alteration in Nutrition Less than body requirements
PRE-OP (ASAP)
- Strict NPO (Allow non-nutritive sucking)
- Parenteral fluid / TPN as necessary (based on weight)
- Nursing responsibilities: Higher amount of glucose, vitamins, minerals. Risk of developing hyperglycemia so CBG
POST-OP
- Breastmilk / Formula via Gastrostomy tube
- Prevent aspiration: Suction as necessary
- Humidified O2 – liquefy thick secretion
SURGICAL MANAGEMENT:
- Staging followed by end to end Anastomosis
1. Cervical Esophagostomy & Gastrostomy insertion
2. Surgical Correstion by ligating the TEF = Reanastomosing the Esophageal ends; repair done in stages
INTUSSUSCEPTION (SMALLER INTESTINE)
- Idiopathic hypertrophy lymphoid tissue 2º to viral infxn pathological lead pt. – POLYP, LYMPHOMA or Meckel Diverticulum Ileocecal valve (ILEOCECAL) ileum invaginates @ cecum & colon
- Hyperactive Portion of SI invaginates into the lumen of another
SYMPTOMS:
- Blood mixes with stool: currant jelly like feces
- Spasmodic abdominal pain
- Blood with mucous in the stool
- Vomiting of bile-stained vomitus (greenish)
- Palpable Sausage Shaped mass
DIAGNOSTIC TEST IS ALSO THE TX:
- BARIUM HYDROSTATIC REDUCTION TECHNIQUE: B. Enema both diagnostic & therapeutic. Introduction of Barium under pressure through rectal catheter. It will not work if there is presence of adhesions. Coiled Spring appearance
- SURGICAL EMERGENCY because POTENTIAL FOR PERFORATION PERITONITIS like suspected APPENDICITIS
HIRSHSPRUNG’S DISEASE / CONGENITAL AGANGLIONIC MEGACOLON / AGANGLIONOSIS
CLASSIC PROFILE
- SPIDER TELANGIECTASIS: Upper Abdomen (smaller veins)
- STRIA: Lower abdomen (stretch marks)
SYMPTOMS
- Delayed Meconium (earliest sign in nursery)
DIAGNOSIS
- RECTAL BIOPSY = To know extent → Barium enema is also given
- Early diagnosis: Good health → corrective surgery
Poor health → palliative management → minor surgery
TREATMENT
- Temporary COLOSTOMY to promote elimination w/ regular COLONIC IRRIGATION using NSS
- Give stool softener
- Modified Diet: Low residue diet (fruits, fresh vegetables), mashed foods because it will facilitate easy passage to colostomy tube. Do not give fiber → will increase bulk of stool (absorbs more fluid).
SURGICAL TREATMENT
- Child weighs 9 kg (20 lbs)
- SUAVE ENDORECTAL PULL THROUGH: pull-down of the normal bowel through muscular sleeve.
- Other procedures: SWENSON, BOLEY, DUHAMEL
PSYCHOGENIC MEGACOLON
- Psychological / no treatment: rooted in the anal phase / toilet training years / control of urine. Adults can have it.
IMPERFORATE ANUS
- Failure of membrane separating rectum from anus
SIGNS & SYMPTOMS:
- No meconium at all
- Inability to insert catheter
- Abdominal distention
For Females: RECTOVAGINAL FISTULA: urine is greenish and foul smelling due to Meconium.
For Males: RECTOVESICAL FISTULA: urine is greenish and foul smelling due to Meconium.
SURGICAL TREATMENT
Consideration on Growth & development
- 1’st Stage:
at nursery do palliative care, Temporary colostomy is done to evacuate feces. - 2’nd Stage
Infant at 10 months old
Readmitted again 1st phase Anoplasty VS. 2nd phase Pullthrough - 3’rd Stage:
After 6 months closure of colostomy & child could already feel the “urge”. There should also be bowel training.
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